The aim of the treatment is to stop the course of the disease or at least to slow it down. The growth of connective tissue (fibrosis) must be stopped. If a underlying disease has been diagnosed, it must be treated. Corresponding risk factors (e.g. smoking, contact with pollutants) must be minimized. This can mean that you have to change your profession (for example, with an activity in the chemical industry).
Because inflammation is often present, it is curbed with special drugs. Some medicines decrease the reaction of the immune system (immunosuppressive drugs). The most famous one here is cortisone. This can either be inhaled directly or taken in form of injection and/or tablets. A new active substance with the name Pirfendion acts against inflammation and at the same time against new formation of connective tissue.
If the oxygen content in the blood becomes too low, the patients are given a probe with the vital gas for several hours. If all treatment measures have not taken effect and the pulmonary fibrosis is very advanced, a lung transplant is the last resort.